Perivascular epitheloid cell tumor (PEComa) mimicking retroperitoneal liposarcoma
نویسندگان
چکیده
منابع مشابه
Perivascular epitheloid cell tumor (PEComa) mimicking retroperitoneal liposarcoma
PEComas are a collection of generally rare tumors, defined by the World Health Organization as 'mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epitheloid cells'. We describe the case of retroperitoneal PEComa with a liposarcoma-like appearance on cross-sectional imaging, but distinctive immunohistochemistry revealing the correct diagnosis.
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Perivascular epithelioid cell tumors (PEComas) are mesenchymal tumors composed of histologically, immunohistochemically, ultrastructurally, and genetically distinctive cells. PEComas have been described in different organs and are considered ubiquitous tumors. In this review we discuss recent informations related to PEComas in the genitourinary tract.
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ژورنال
عنوان ژورنال: World Journal of Surgical Oncology
سال: 2014
ISSN: 1477-7819
DOI: 10.1186/1477-7819-12-3